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Case Report
Unique association of Lhermitte–Duclos disease and frontal encephalocele
1 Department of Neuroradiology, Ibn Sina Hospital, Mohamed V University, Rabat, Morocco
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Habib Bellamlih
Ibn Sina Hospital, Mohamed V University, Rabat,
Morocco
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Article ID: 101041Z01HB2019
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Bellamlih H, El Farouki A, El Hassani MR, Jiddane M, Fikri M. Unique association of Lhermitte–Duclos disease and frontal encephalocele. Int J Case Rep Images 2019;10:101041Z01HB2019.ABSTRACT
Lhermitte–Duclos disease, also known as dysplastic gangliocytoma of the cerebellum, is an extremely rare cerebellar tumor characterized by an enlargement of cerebellar folia. Its etiology remains controversial. Imaging modalities, especially magnetic resonance imaging, contribute to establish a correct and accurate diagnosis with pre and postoperative assessment. The characteristic “tiger striping” appearance is pathognomonic. The recognition of this unusual and benign condition is particularly important, given the possible association with Cowden’s syndrome and therefore the need to identify concurrent malignancies.To our knowledge, we describe a rare and unique presentation of histologically proven Lhermitte–Duclos disease associated with a frontal encephalocele surgically treated.
Keywords: Dysplastic gangliocytoma, Frontal encephalocele, Lhermitte–Duclos disease, Magnetic resonance imaging
SUPPORTING INFORMATION
Author Contributions
Habib Bellamlih - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Aymane El Farouki - Substantial contributions to conception and design, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Moulay Rachid El Hassani - Substantial contributions to conception and design, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Mohammed Jiddane - Substantial contributions to conception and design, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Meriem Fikri - Substantial contributions to conception and design, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Source of SupportNone
Data AvailabilityAll relevant data are within the paper and its Supporting Information files.
Conflict of InterestAuthors declare no conflict of interest.
Copyright© 2019 Habib Bellamlih et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.
