 |
Case Report
Budd–Chiari syndrome complicating hepatic sarcoidosis: A rare association
1 Emergency Radiology Department, Ibn Sina Hospital, CHU of Rabat, Morocco
Address correspondence to:
Saoud Aida
Secteur 15, bloc D n°19, Hay Riad, Rabat,
Morocco
Message to Corresponding Author
Article ID: 101068Z01SA2019
Access full text article on other devices
Access PDF of article on other devices
How to cite this article
Aida S, Habib B, Zahra LF. Budd–Chiari syndrome complicating hepatic sarcoidosis: A rare association. Int J Case Rep Images 2019;10:101068Z01SA2019.ABSTRACT
Introduction: The Budd–Chiari syndrome is an obstruction of the hepatic venous drainage. It is not common as a complication of hepatic sarcoidosis but the association is possible. We report a case of Budd–Chiari syndrome complicating a hepatic sarcoidosis.
Case Report: A 32-year-old female patient with a history of mediastino-pulmonary, hepatic, and splenic sarcoidosis since her young age, that stopped her medication, was readmitted at our Emergency Department for recurrent threatening hematemesis. The oesogastroduodenal fibroscopy found esophageal varices. Biological assessment found a cytolysis and cholestasis. Hepatic Doppler ultrasound showed nodular bumpy hepatomegaly, with outflow obstruction of the hepatic veins, and a laminated aspect of the inferior vena cava that remains permeable. Abdominal computed tomography (CT) showed multinodular liver and spleen, multiple lymphadenopathies, and a lack of individualization of hepatic veins. Chest CT showed an interstitial syndrome associated with bilateral mediastinal and hilar adenopathies. Viral serologies B and C, and the search for thrombophilia were negative. Hepatic sarcoidosis was previously confirmed by liver biopsy, with a negative tuberculosis testing and a high level of angiotensin-converting enzyme. All these assessments led to the diagnosis of Budd–Chiari syndrome complicating hepatic sarcoidosis.
Conclusion: Budd–Chiari syndrome is thus an exceptional complication, but possible in case of hepatic sarcoidosis. Therefore, it is worthwhile to look for it in case of any worsening of hepatic sarcoidosis, and to suggest possible sarcoidosis in case of Budd–Chiari syndrome.
Keywords: Budd–Chiari syndrome, Hepatic sarcoidosis, Liver, Sarcoidosis
SUPPORTING INFORMATION
Author Contributions
Saoud Aida - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Final approval of the version to be published
Bellamlih Habib - Analysis of data, Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published
Laamrani Fatima Zahra - Analysis of data, Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published
Guaranter of SubmissionThe corresponding author is the guarantor of submission.
Source of SupportNone
Consent StatementWritten informed consent was obtained from the patient for publication of this article.
Data AvailabilityAll relevant data are within the paper and its Supporting Information files.
Conflict of InterestAuthors declare no conflict of interest.
Copyright© 2019 Saoud Aida et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.
